Renal graft failure due to type 1 primary hyperoxaluria.
نویسندگان
چکیده
Primary hyperoxaluria type 1 (PH1) usually presents with recurrent urolithiasis, nephrocalcinosis and progressive renal failure at a relatively young age. This report describes a patient who, due to the late onset of end-stage renal disease, had been diagnosed with PH1 only after failure of his second kidney graft. Retrospectively, his vascular problems, skeletal abnormalities and cardiac arrhythmias fit the picture of severe systemic oxalosis. Possible therapeutic options are discussed.
منابع مشابه
Primary hyperoxaluria: a rare but important cause of nephrolithiasis.
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ورودعنوان ژورنال:
- The Netherlands journal of medicine
دوره 60 10 شماره
صفحات -
تاریخ انتشار 2002